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Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl

dc.creatorHalpert, Evelyne
dc.creatorFigueroa, Juan Luis
dc.creatorRojas, Armando
dc.creatorOrtiz, Clara Ines
dc.creatorChaparro, Daniela
dc.creatorGalindo, Marcela
dc.creatorLammoglia, Juan Javier
dc.creatorRumie, Carolina
dc.creatorOlmos, Carlos
dc.creator.googleHalpert, Evelynespa
dc.creator.googleFigueroa, Juan Luisspa
dc.creator.googleRojas, Armandospa
dc.creator.googleOrtiz, Clara Inesspa
dc.creator.googleChaparro, Danielaspa
dc.creator.googleGalindo, Marcelaspa
dc.creator.googleLammoglia, Juan Javierspa
dc.creator.googleRumie, Carolinaspa
dc.creator.googleOlmos, Carlosspa
dc.date.accessioned2019-01-31T14:46:18Z
dc.date.available2019-01-31T14:46:18Z
dc.date.created2016
dc.date.issued2016
dc.description.abstractIntroduction: Paraneoplastic pemphigus is an autoimmune disease associated with an underlying tumor. Several cases have been reported as unusual pemphigus vulgaris, erythema multiforme, or paraneoplastic bullous disease,1 but the incidence of the condition is unknown.2 Response to treatment is generally poor, with significant morbidity and mortality. This condition is clinically characterized by severe mucositis and polymorphic blistering skin eruptions, and histologically by acantholysis, keratinocyte necrosis, and interface dermatitis.3 Immunoprecipitation and immunoblot testing detect autoantibodies against desmosomal polypeptides.4 We describe a case of paraneoplastic pemphigus associated with an abdominal inflammatory myofibroblastic tumor in a 7-year-old girl.eng
dc.format.mimetypeapplication/pdf
dc.identifier.issnISSN 2352-5126
dc.identifier.urihttp://repository.urosario.edu.co/handle/10336/18971
dc.language.isoengspa
dc.relation.citationEndPage40
dc.relation.citationIssueNo. 1
dc.relation.citationStartPage37
dc.relation.citationTitleJAAD Case Reports
dc.relation.citationVolumeVol. 2
dc.relation.ispartofJAAD Case Reports, ISSN: 2352-5126, Vol. 2/No. 1 (2016) pp. 37-40spa
dc.relation.urihttps://www.jaadcasereports.org/article/S2352-5126(15)00174-5/pdfspa
dc.rights.accesRightsinfo:eu-repo/semantics/openAccess
dc.rights.accesoAbierto (Texto Completo)spa
dc.rights.cchttps://creativecommons.org/licenses/by-nc-nd/4.0/spa
dc.source.bibliographicCitationAnhalt, G.J., Paraneoplastic pemphigus (1997) Adv Dermatol, 12, pp. 77-96spa
dc.source.instnameinstname:Universidad del Rosario
dc.source.reponamereponame:Repositorio Institucional EdocUR
dc.subjectMyofibroblastic Tumorspa
dc.subjectParaneoplastic Syndromesspa
dc.subjectPediatricsspa
dc.subjectPemphigus Vulgarisspa
dc.subject.ddcEnfermedadesspa
dc.subject.decsAzathioprinespa
dc.subject.decsMethylprednisolonespa
dc.subject.decsOxacillinspa
dc.subject.decsPrednisonespa
dc.subject.decsRituximabspa
dc.subject.decsThalidomidespa
dc.subject.decsArticlespa
dc.subject.decsCase Reportspa
dc.subject.decsCataractspa
dc.subject.decsChildspa
dc.subject.decsColombiaspa
dc.subject.decsCushing Syndromespa
dc.subject.decsDepressionspa
dc.subject.decsFemalespa
dc.subject.decsHospitalizationspa
dc.subject.decsHumanspa
dc.subject.decsImmunofluorescencespa
dc.subject.decsMedical Historyspa
dc.subject.decsMouth Ulcerspa
dc.subject.decsMyopathyspa
dc.subject.decsParaneoplastic Pemphigusspa
dc.subject.decsPemphigus Vulgarisspa
dc.subject.decsPlasma Cell Granulomaspa
dc.subject.decsPriority Journalspa
dc.subject.decsPsychotherapyspa
dc.subject.decsSchool Childspa
dc.subject.decsSkin Biopsyspa
dc.subject.decsSkin Defectspa
dc.subject.decsSkin Infectionspa
dc.subject.lembEnfermedades autoinmunesspa
dc.subject.lembEritema multiformespa
dc.subject.lembPénfigospa
dc.titleInflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girlspa
dc.typearticleeng
dc.type.hasVersioninfo:eu-repo/semantics/publishedVersion
dc.type.spaArtículospa
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