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Incidental finding of pulmonary arterial sling during patent ductus arteriosus surgery in a patient with Mowat-Wilson syndrome

dc.creatorCano Sierra J.D.spa
dc.creatorMestra C.F.spa
dc.creatorRonderos Dumit M.A.spa
dc.date.accessioned2020-05-26T00:03:55Z
dc.date.available2020-05-26T00:03:55Z
dc.date.created2018spa
dc.description.abstractMowat-Wilson syndrome is a genetic condition due to a mutation in the ZEB2 gene; it affects many systems including the cardiovascular system. The pulmonary arterial sling originates from a failure of development of the proximal portion of the left sixth aortic arch, resulting in an anomalous left pulmonary artery origin from the posterior wall of the right pulmonary artery and the left pulmonary artery crossing to the left lung between the trachea and the oesophagus. We present a 4-month-old infant with Mowat-Wilson syndrome and left pulmonary arterial sling, and discuss the association of these two rare conditions. Pulmonary arterial sling is significantly more frequent in patients with Mowat-Wilson syndrome than in the general population. © Cambridge University Press 2018.eng
dc.format.mimetypeapplication/pdf
dc.identifier.doihttps://doi.org/10.1017/S1047951118000689
dc.identifier.issn10479511
dc.identifier.issn14671107
dc.identifier.urihttps://repository.urosario.edu.co/handle/10336/23640
dc.language.isoengspa
dc.publisherCambridge University Pressspa
dc.relation.citationEndPage1076
dc.relation.citationIssueNo. 8
dc.relation.citationStartPage1074
dc.relation.citationTitleCardiology in the Young
dc.relation.citationVolumeVol. 28
dc.relation.ispartofCardiology in the Young, ISSN:10479511, 14671107, Vol.28, No.8 (2018); pp. 1074-1076spa
dc.relation.urihttps://www.scopus.com/inward/record.uri?eid=2-s2.0-85049300172&doi=10.1017%2fS1047951118000689&partnerID=40&md5=ca09a4484be74e1028af10b7fb276a92spa
dc.rights.accesRightsinfo:eu-repo/semantics/openAccess
dc.rights.accesoAbierto (Texto Completo)spa
dc.source.instnameinstname:Universidad del Rosariospa
dc.source.reponamereponame:Repositorio Institucional EdocURspa
dc.subject.keywordAnamnesisspa
dc.subject.keywordx-ray computedeng
dc.subject.keywordArticlespa
dc.subject.keywordBronchoscopyspa
dc.subject.keywordCase reportspa
dc.subject.keywordClinical articlespa
dc.subject.keywordEchocardiographyspa
dc.subject.keywordFailure to thrivespa
dc.subject.keywordGastroesophageal refluxspa
dc.subject.keywordGenespa
dc.subject.keywordGenetic disorderspa
dc.subject.keywordHeart dilatationspa
dc.subject.keywordHumanspa
dc.subject.keywordImage reconstructionspa
dc.subject.keywordIncidental findingspa
dc.subject.keywordInfantspa
dc.subject.keywordIntensive care unitspa
dc.subject.keywordMalespa
dc.subject.keywordMowat wilson syndromespa
dc.subject.keywordPatent ductus arteriosusspa
dc.subject.keywordPhysical examinationspa
dc.subject.keywordPulmonary arterial slingspa
dc.subject.keywordPulmonary arteryspa
dc.subject.keywordPulmonary artery malformationspa
dc.subject.keywordSequence analysisspa
dc.subject.keywordSystolic heart murmurspa
dc.subject.keywordTime to treatmentspa
dc.subject.keywordX-ray computed tomographyspa
dc.subject.keywordZeb2 genespa
dc.subject.keywordAbnormalitiesspa
dc.subject.keywordComplicationspa
dc.subject.keywordDiagnostic imagingspa
dc.subject.keywordFaciesspa
dc.subject.keywordGeneticsspa
dc.subject.keywordHirschsprung diseasespa
dc.subject.keywordIncidental findingspa
dc.subject.keywordIntellectual impairmentspa
dc.subject.keywordMicrocephalyspa
dc.subject.keywordPatent ductus arteriosusspa
dc.subject.keywordThree dimensional imagingspa
dc.subject.keywordVascular surgeryspa
dc.subject.keywordDuctus arteriosuseng
dc.subject.keywordFaciesspa
dc.subject.keywordHirschsprung diseasespa
dc.subject.keywordHumansspa
dc.subject.keywordImagingeng
dc.subject.keywordIncidental findingsspa
dc.subject.keywordInfantspa
dc.subject.keywordIntellectual disabilityspa
dc.subject.keywordMalespa
dc.subject.keywordMicrocephalyspa
dc.subject.keywordPulmonary arteryspa
dc.subject.keywordTomographyeng
dc.subject.keywordVascular surgical proceduresspa
dc.subject.keyword6th aortic archspa
dc.subject.keywordGeneral cardiologyspa
dc.subject.keywordMowat-wilson syndromespa
dc.subject.keywordPulmonary arterial slingspa
dc.subject.keywordZeb2spa
dc.titleIncidental finding of pulmonary arterial sling during patent ductus arteriosus surgery in a patient with Mowat-Wilson syndromespa
dc.typearticleeng
dc.type.hasVersioninfo:eu-repo/semantics/publishedVersion
dc.type.spaArtículospa
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