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Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.

dc.creatorHalpert, Evelynespa
dc.creatorFigueroa, Juan Luisspa
dc.creatorRojas, Armandospa
dc.creatorOrtiz, Clara Inesspa
dc.creatorChaparro, Danielaspa
dc.creatorGalindo, Marcelaspa
dc.creatorLammoglia, Juan Javierspa
dc.creatorRumie, Carolinaspa
dc.creatorOlmos, Carlosspa
dc.date.accessioned2020-08-06T16:20:19Z
dc.date.available2020-08-06T16:20:19Z
dc.date.created2016-01-26spa
dc.description.abstractParaneoplastic pemphigus is an autoimmune disease associated with an underlying tumor. Several cases have been reported as unusual pemphigus vulgaris, erythema multiforme, or paraneoplastic bullous disease,1 but the incidence of the condition is unknown.2 Response to treatment is generally poor, with significant morbidity and mortality. This condition is clinically characterized by severe mucositis and polymorphic blistering skin eruptions, and histologically by acantholysis, keratinocyte necrosis, and interface dermatitis.3 Immunoprecipitation and immunoblot testing detect autoantibodies against desmosomal polypeptides.4 We describe a case of paraneoplastic pemphigus associated with an abdominal inflammatory myofibroblastic tumor in a 7-year-old girl.eng
dc.format.mimetypeapplication/pdf
dc.identifier.doihttps://doi.org/10.1016/j.jdcr.2015.10.009
dc.identifier.issnISSN: 2352-5126
dc.identifier.urihttps://repository.urosario.edu.co/handle/10336/25961
dc.language.isoengspa
dc.publisherElsevierspa
dc.relation.citationEndPage40
dc.relation.citationIssueNo. 1
dc.relation.citationStartPage37
dc.relation.citationTitleJAAD case reports
dc.relation.citationVolumeVol. 2
dc.relation.ispartofJAAD case reports, ISSN: 2352-5126, Vol.2, No.1 (January, 2016); pp.37-40spa
dc.relation.urihttps://www.jaadcasereports.org/article/S2352-5126(15)00174-5/fulltextspa
dc.rights.accesRightsinfo:eu-repo/semantics/openAccess
dc.rights.accesoAbierto (Texto Completo)spa
dc.sourceJAAD case reportsspa
dc.source.instnameinstname:Universidad del Rosario
dc.source.reponamereponame:Repositorio Institucional EdocUR
dc.subject.keywordMyofibroblastic tumorspa
dc.subject.keywordParaneoplastic syndromesspa
dc.subject.keywordPemphigus vulgarisspa
dc.subject.keywordPediatricsspa
dc.titleInflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.spa
dc.title.TranslatedTitleTumor miofibroblástico inflamatorio que se presenta como pénfigo paraneoplásico en una niña de 7 años.spa
dc.typearticleeng
dc.type.hasVersioninfo:eu-repo/semantics/publishedVersion
dc.type.spaArtículospa
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