Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.

Halpert, Evelyne; Figueroa, Juan Luis; Rojas, Armando; Ortiz, Clara Ines; Chaparro, Daniela; Galindo, Marcela; Lammoglia, Juan Javier; Rumie, Carolina; Olmos, Carlos

doi:https://doi.org/10.1016/j.jdcr.2015.10.009

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Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.

https://repository.urosario.edu.co/handle/10336/25961
https://doi.org/10.1016/j.jdcr.2015.10.009

Autores

Halpert, Evelyne

Figueroa, Juan Luis

Rojas, Armando

Ortiz, Clara Ines

Chaparro, Daniela

Galindo, Marcela

Lammoglia, Juan Javier

Rumie, Carolina

Olmos, Carlos

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Fecha

2016-01-26

Editor

Elsevier

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Abstract

Paraneoplastic pemphigus is an autoimmune disease associated with an underlying tumor. Several cases have been reported as unusual pemphigus vulgaris, erythema multiforme, or paraneoplastic bullous disease,1 but the incidence of the condition is unknown.2 Response to treatment is generally poor, with significant morbidity and mortality. This condition is clinically characterized by severe mucositis and polymorphic blistering skin eruptions, and histologically by acantholysis, keratinocyte necrosis, and interface dermatitis.3 Immunoprecipitation and immunoblot testing detect autoantibodies against desmosomal polypeptides.4 We describe a case of paraneoplastic pemphigus associated with an abdominal inflammatory myofibroblastic tumor in a 7-year-old girl.